perinatologyРоссийский вестник перинатологии и педиатрииRossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics)1027-40652500-2228Ltd. “The National Academy of Pediatric Science and Innovation”10.21508/1027-4065-2021-66-6-23-32perinatology-1525Research ArticleОБЗОРЫ ЛИТЕРАТУРЫLITERATURE REVIEWSДиагностика легочной гипертензии, ассоциированной с врожденными пороками сердца. Часть 2. ЭхокардиографияDiagnosis of pulmonary hypertension associated with congenital heart disease. Part 2. Echocardiographyhttps://orcid.org/0000-0001-9445-836XБарышниковаИ. Ю.BaryshnikovaI. Yu.

Барышникова Ирина Юрьевна – к.м.н., науч. сотр., доц. кафедры сердечно-сосудистой хирургии с курсом аритмологии и клинической электрофизиологии Института подготовки кадров высшей квалификации и профессионального образования; врач ультразвуковой диагностики

121552 Москва, Рублевское шоссе, 135

Moscow

jatropha@mail.ruhttps://orcid.org/0000-0001-8937-1796ШмальцА. А.ShmaltsA. A.

Шмальц Антон Алексеевич – д.м.н., вед. науч. сотр. отделения хирургического лечения заболеваний сердца с прогрессирующей легочной гипертензией; доц. кафедры сердечно-сосудистой хирургии

121552 Москва, Рублевское шоссе, 135

Moscow

ФГБУ «Национальный медицинский исследовательский центр сердечно-сосудистой хирургии им. А.Н. Бакулева» Минздрава России; ФГБУ «Национальный медицинский исследовательский центр акушерства, гинекологии и перинатологии им. В.И. Кулакова» Минздрава РоссииРоссияBakoulev National Medical Research Center for Cardiovascular Surgery; Kulakov National Medical Research Center for Obstetrics, Gynecology and PerinatologyRussian FederationФГБУ «Национальный медицинский исследовательский центр сердечно-сосудистой хирургии им. А.Н. Бакулева» Минздрава России; ФГБОУ ДПО «Российская медицинская академия непрерывного профессионального образования» Минздрава РоссииРоссияBakoulev National Medical Research Center for Cardiovascular Surgery; Russian Medical Academy of Continuing Professional EducationRussian Federation2021190120226662332Copyright © Ltd. “The National Academy of Pediatric Science and Innovation”, 20222022Ltd. “The National Academy of Pediatric Science and Innovation”Ltd. “The National Academy of Pediatric Science and Innovation”https://www.ped-perinatology.ru/jour/about/submissions#copyrightNoticehttps://www.ped-perinatology.ru/jour/article/view/1525

Согласно действующим российским, евразийским и европейским рекомендациям по легочной гипертензии у детей и взрослых, а также рекомендациям 6-го Всемирного симпозиума по легочной гипертензии, основными эхокардиографическими показателями при оценке идиопатической и схожих форм легочной гипертензии служат расчетное систолическое, диастолическое и среднее давление в легочной артерии, соотношение размеров правого и левого желудочков сердца, индекс эксцентричности левого желудочка, систолическая экскурсия фиброзного кольца трикуспидального клапана, систолическое движение миокарда на уровне фиброзного кольца трикуспидального клапана и площадь правого предсердия. В обзоре рассматриваются возможности и ограничения современной эхокардиографии в диагностике легочной гипертензии, ассоциированной с врожденными пороками сердца.

The calculated systolic, diastolic and mean pulmonary artery pressure, the ratio of the sizes of the right and left ventricles of the heart, the eccentricity index of the left ventricle, systolic excursion of the fibrous ring of the tricuspid valve, systolic movement of the myocardium at the level of the fibrous ring of the tricuspid valve and the area of the right atrium are the main echocardiographic indicators for assessing idiopathic and similar forms of pulmonary hypertension according to the current Russian, Eurasian and European guidelines for pulmonary hypertension in children and adults, as well as the recommendations of the 6th World Symposium on Pulmonary Hypertension. The article explores the possibilities and limitations of modern echocardiography in the diagnosis of pulmonary hypertension associated with congenital heart defects.

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The authors declare that there are no conflicts of interest present.