perinatologyРоссийский вестник перинатологии и педиатрииRossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics)1027-40652500-2228Ltd. “The National Academy of Pediatric Science and Innovation”10.21508/1027-4065-2016-61-5-155-159perinatology-399Research ArticleXIII РОССИЙСКАЯ КОНФЕРЕНЦИЯ «ПЕДИАТРИЯ И ДЕТСКАЯ ХИРУРГИЯ В ПРИВОЛЖСКОМ ФЕДЕРАЛЬНОМ ОКРУГЕ»13TH RUSSIAN CONFERENCE ON PEDIATRICS AND PEDIATRIC SURGERY IN THE VOLGA FEDERAL DISTRICTДиагностика и лечение гепатопульмонального синдрома у детейHepatopulmonary syndrome in pediatric patients (clinical presentation)КамаловаА. А.KamalovaA. A.

кафедра госпитальной педиатрии с курсом поликлинической педиатрии 

д.м.н., доцент 

профессор 

420012 Казань, ул. Бутлерова, д. 36’

ШакироваА. Р.ShakirovaA. R.

кафедра госпитальной педиатрии с курсом поликлинической педиатрии 

асс. кафедры 

420012 Казань, ул. Бутлерова, д. 36’

ГБОУ ВПО «Казанский государственный медицинский университет» Минздрава России; ГБОУ ДПО «Казанская государственная медицинская академия» Минздрава России, КазаньРоссияKazan State Medical University; Kazan State Medical Academy, KazanRussian FederationГБОУ ДПО «Казанская государственная медицинская академия» Минздрава России, КазаньРоссияKazan State Medical Academy, KazanRussian Federation201620112016615155159Copyright © Ltd. “The National Academy of Pediatric Science and Innovation”, 20162016Ltd. “The National Academy of Pediatric Science and Innovation”Ltd. “The National Academy of Pediatric Science and Innovation”https://www.ped-perinatology.ru/jour/about/submissions#copyrightNoticehttps://www.ped-perinatology.ru/jour/article/view/399

Гепатопульмональный синдром — редкое осложнение заболеваний печени, ведущее к нарушению перфузии легких и снижению оксигенации крови. Обсуждаются вопросы диагностики и лечения этого синдрома. Представлено собственное наблюдение 11-летнего ребенка с врожденным фиброзом печени и гепатопульмональным синдромом. 

Hepatopulmonary syndrome (HPS) is a rare complication of liver diseases, resulting in lung perfusion disturbances and reduction of blood oxygenation. We report a case of hepatopulmonary syndrome in an 11- year-old-boy with congenital liver fibrosis. 

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The authors declare that there are no conflicts of interest present.