perinatologyРоссийский вестник перинатологии и педиатрииRossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics)1027-40652500-2228Ltd. “The National Academy of Pediatric Science and Innovation”perinatology-51Research ArticleОБЗОР ЛИТЕРАТУРЫREVIEWSСовременные методы обследования больных гипертрофической кардиомиопатиейCurrent examination methods in patients with hypertrophic cardiomyopathyГрозноваО. С.GroznovaO. S.

д.м.н., в.н.с. отделения патологии сердечно-сосудистой системы

ЛеонтьеваИ. В.LeontyevaI. V.

д.м.н. проф., зав.  отделением патологии сердечно-сосудистой системы

ПоляковаА. В.PolyakovaA. V.

биолог лаборатории молекулярной и биохимической диагностики

Научно-исследовательский клинический институт педиатрии, МоскваРоссияResearch Clinical Institute of Pediatrics, MoscowRussian Federation2014030320165942327Copyright © Ltd. “The National Academy of Pediatric Science and Innovation”, 20162016Ltd. “The National Academy of Pediatric Science and Innovation”Ltd. “The National Academy of Pediatric Science and Innovation”https://www.ped-perinatology.ru/jour/about/submissions#copyrightNoticehttps://www.ped-perinatology.ru/jour/article/view/51

Высокая частота встречаемости гипертрофии миокарда ставит перед практическими врачами задачу дифференциального диагноза и раннего выявления среди пациентов с гипертрофией миокарда больных гипертрофической кардиомиопатией для определения тактики ведения, предотвращения жизнеугрожающих состояний и улучшения прогноза. В статье освещены современные подходы к диагностике гипертрофических кардиомиопатий. представлены молекулярно-генетические исследования; 3D эхокардиография, позволяющая точно измерить объемные показатели камер сердца; спекл-трекинг и оценка деформации левого предсердия и левого желудочка как диагностические и прогностические критерии течения гипертрофической кардиомиопатии; МРТ сердца с определением объемных показателей, массы миокарда и трабекулярности левого желудочка; биохимические маркеры перегрузки предсердий (мозговые натрийуретические пептиды В-типа) и ишемии миокарда (тропонин-Т); а также электрокардиографические методы исследования. 

The high incidence of myocardial hypertrophy poses practitioners a problem in the differential diagnosis and early detection of patients with hypertrophic cardiomyopathy among those with myocardial hypertrophy in order to define treatment policy, to prevent life-threating conditions, and to improve prognosis. The paper presents current approaches to diagnosing hypertrophic cardiomyopathies and molecular genetic studies; 3D echocardiography that allows the accurate measurement of the volume parameters of cardiac chambers; speckle tracking and assessment of left atrial and left ventricular strain as diagnostic and prognostic criteria for the course of hypertrophic cardiomyopathy; cardiac MRI and determination of the volume parameters, myocardial mass, and trabecular pattern of the left ventricle; biochemical parameters of atrial overload (B-type or brain natriuretic peptides) and myocardial ischemia (troponin T), as well as electrocardiographic studies. 

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The authors declare that there are no conflicts of interest present.