perinatologyРоссийский вестник перинатологии и педиатрииRossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics)1027-40652500-2228Ltd. “The National Academy of Pediatric Science and Innovation”10.21508/1027-4065-2018-63-5-167-171perinatology-744Research ArticleСЛУЧАЙ ИЗ ПРАКТИКИCASE REPORTSСЛОЖНОСТЬ ДИАГНОСТИКИ ИДИОПАТИЧЕСКОЙ ЛЕГОЧНОЙ АРТЕРИАЛЬНОЙ ГИПЕРТЕНЗИИTHE COMPLEXITY OF DIAGNOSING IDIOPATHIC PULMONARY ARTERIAL HYPERTENSIONСадыковаД. И.SadykovaD. I.

д.м.н., проф., зав. кафедрой педиатрии с курсом поликлинической педиатрии.

СабироваД. Р.SabirovaD. R.

к.м.н., доц. кафедры педиатрии с курсом поликлинической педиатрии.

КустоваН. В.KustovaN. V.

аспирант кафедры педиатрии с курсом поликлинической педиатрии.

ФирсоваН. Н.FirsovaN. N.

зав. кардиологическим отделением.

ХуснуллинаГ. А.KhusnullinaG. A.

к.м.н., врач кардиологического отделения.

420138 Казань, Оренбургский тракт, д. 140.

Казанская государственная медицинская академия – филиал ФГБОУ ДПО РМАНПО Минздрава России.РоссияKazan State Medical Academy – branch of the Russian Medical Academy of Post-Graduate Education.Russian FederationГАУЗ Детская республиканская клиническая больница Минздрава Республики Татарстан.РоссияChildren’s Republican Clinical Hospital of Tatarstan Republic.Russian Federation201820112018635167171Copyright © Ltd. “The National Academy of Pediatric Science and Innovation”, 20182018Ltd. “The National Academy of Pediatric Science and Innovation”Ltd. “The National Academy of Pediatric Science and Innovation”https://www.ped-perinatology.ru/jour/about/submissions#copyrightNoticehttps://www.ped-perinatology.ru/jour/article/view/744

Идиопатическая легочная артериальная гипертензия – прогрессирующее, на сегодняшний день неизлечимое заболевание неясной этиологии, характеризующееся интенсивным ремоделированием легочного сосудистого русла с преимущественным поражением дистальных легочных артерий и артериол. Диагностическим критерием заболевания является повышение среднего давления в легочной артерии более 25 мм рт. ст. Диагностировать легочную гипертензию, особенно на ранних этапах, очень сложно, так как клинические симптомы неспецифичны. Приведено описание клинического случая диагностики и лечения ребенка с первичной легочной гипертензией высокой степени.

Idiopathic pulmonary arterial hypertension is a progressive, incurable disease of unclear etiology; it is characterized by intensive remodeling of the pulmonary vascular bed with a predominant lesion of the distal pulmonary arteries and arterioles. A diagnostic criterion of the disease is an increase in the average pressure in the pulmonary artery more than 25 mm Hg. Arterial hypertension is difficult to diagnose, especially at the early stages due to non-specific clinical symptoms. The article describes the clinical case of diagnostics and treatment of a child with primary pulmonary hypertension of high degree.

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The authors declare that there are no conflicts of interest present.