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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">perinatology</journal-id><journal-title-group><journal-title xml:lang="ru">Российский вестник перинатологии и педиатрии</journal-title><trans-title-group xml:lang="en"><trans-title>Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics)</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">1027-4065</issn><issn pub-type="epub">2500-2228</issn><publisher><publisher-name>Ltd. “The National Academy of Pediatric Science and Innovation”</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.21508/1027-4065-2019-64-5-194-198</article-id><article-id custom-type="elpub" pub-id-type="custom">perinatology-991</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>ОРИГИНАЛЬНЫЕ СТАТЬИ</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>ORIGINAL ARTICLES</subject></subj-group></article-categories><title-group><article-title>Особенности нутритивного статуса у детей с врожденными пороками сердца</article-title><trans-title-group xml:lang="en"><trans-title>The features of nutritional status in children with congenital heart disease</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0002-6662-3548</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Садыкова</surname><given-names>Д. И.</given-names></name><name name-style="western" xml:lang="en"><surname>Sadykova</surname><given-names>D. I.</given-names></name></name-alternatives><bio xml:lang="ru"><p>д.м.н., проф., зав. кафедрой госпитальной педиатрии,</p><p>420011 Казань, ул. Бутлерова, д. 49</p></bio><bio xml:lang="en"><p>Kazan</p></bio><email xlink:type="simple">sadykovadi@mail.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><contrib-id contrib-id-type="orcid">https://orcid.org/0000-0003-2701-1079</contrib-id><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Хабибрахманова</surname><given-names>З. Р.</given-names></name><name name-style="western" xml:lang="en"><surname>Khabibrakhmanova</surname><given-names>Z. R.</given-names></name></name-alternatives><bio xml:lang="ru"><p>к.м.н., асс. кафедры госпитальной педиатрии,</p><p>420011 Казань, ул. Бутлерова, д. 49</p></bio><bio xml:lang="en"><p>Kazan</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Шакирова</surname><given-names>А. Р.</given-names></name><name name-style="western" xml:lang="en"><surname>Shakirova</surname><given-names>A. R.</given-names></name></name-alternatives><bio xml:lang="ru"><p>зав. отделением педиатрии,</p><p>420138 Казань, ул. Оренбургский тракт, д. 140</p></bio><bio xml:lang="en"><p>Tatarstan</p></bio><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Сафина</surname><given-names>Л. З.</given-names></name><name name-style="western" xml:lang="en"><surname>Safina</surname><given-names>L. Z.</given-names></name></name-alternatives><bio xml:lang="ru"><p>к.м.н., доц. кафедры педиатрии и неонатологии,</p><p>420012 Казань, ул. Муштари, д. 11</p></bio><bio xml:lang="en"><p>Kazan</p></bio><xref ref-type="aff" rid="aff-3"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru"><institution>ФГБОУ ВО «Казанский государственный медицинский университет» Минздрава России</institution><country>Россия</country></aff><aff xml:lang="en"><institution>Kazan State Medical University</institution><country>Russian Federation</country></aff></aff-alternatives><aff-alternatives id="aff-2"><aff xml:lang="ru"><institution>ГАУЗ «Детская республиканская клиническая больница» Минздрава Республики Татарстан</institution><country>Россия</country></aff><aff xml:lang="en"><institution>Children’s Republican Clinical Hospital</institution><country>Russian Federation</country></aff></aff-alternatives><aff-alternatives id="aff-3"><aff xml:lang="ru"><institution>Казанская государственная медицинская академия – филиал ФГБОУ ДПО «Российская медицинская академия непрерывного профессионального образования» Минздрава России</institution><country>Россия</country></aff><aff xml:lang="en"><institution>Kazan State Medical Academy – branch of Russian Medical Academy of Continuing Professional Education</institution><country>Russian Federation</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2019</year></pub-date><pub-date pub-type="epub"><day>15</day><month>11</month><year>2019</year></pub-date><volume>64</volume><issue>5</issue><fpage>194</fpage><lpage>198</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Ltd. “The National Academy of Pediatric Science and Innovation”, 2019</copyright-statement><copyright-year>2019</copyright-year><copyright-holder xml:lang="ru">Ltd. “The National Academy of Pediatric Science and Innovation”</copyright-holder><copyright-holder xml:lang="en">Ltd. “The National Academy of Pediatric Science and Innovation”</copyright-holder><license xlink:href="https://www.ped-perinatology.ru/jour/about/submissions#copyrightNotice" xlink:type="simple"><license-p>https://www.ped-perinatology.ru/jour/about/submissions#copyrightNotice</license-p></license></permissions><self-uri xlink:href="https://www.ped-perinatology.ru/jour/article/view/991">https://www.ped-perinatology.ru/jour/article/view/991</self-uri><abstract><p>Недостаточность питания – частая проблема у детей с врожденными пороками сердца, независимо от типа порока и наличия или отсутствия цианоза. Дети, рожденные с пороками сердца, формируют группу высокого риска развития нутритивного дефицита. Хирургическое лечение врожденных пороков сердца часто сопровождается метаболическими изменениями и повышением потребности в энергии и белке. Коррекция нутритивного статуса у детей с врожденными пороками сердца позволяет улучшить состояние пациентов после кардиохирургических операций. Целью нашего исследования была оценка нутритивного статуса детей, госпитализированных в кардиохирургическое отделение с врожденными пороками сердца, и проведение коррекции энтерального питания. Осуществлен анализ антропометрических данных по Z-score (масса– возраст) детей, поступивших в отделение для обследования и коррекции порока сердца. Сделан вывод о необходимости дальнейших исследований по оценке влияния изменений нутритивного статуса на заболеваемость и летальность пациентов с врожденными пороками сердца и возможности оптимальной коррекции нутритивного статуса.</p></abstract><trans-abstract xml:lang="en"><p>Malnutrition is a common problem in children with congenital heart defects, regardless of the type of defect and the presence / absence of cyanosis. Children born with heart defects form a high-risk group of nutritional deficiency. Surgical treatment of congenital heart defects is often accompanied by metabolic changes and increased needs of energy and protein. Correction of nutritional status in children with congenital heart diseases improves the condition of patients after cardiac surgery. The purpose of our study was to assess the nutritional status of children with congenital heart defects hospitalized to the cardiac surgery department, and to correct their enteral nutrition. The authors analyzed anthropometric data on the Z-score (weight – age) of children admitted to the department for examination and correction of heart disease. The authors concluded that there is need for further studies to assess the impact of changes in nutritional status on the incidence and mortality of patients with congenital heart defects and the possibility of optimal correction of nutritional status.</p></trans-abstract><kwd-group xml:lang="ru"><kwd>дети</kwd><kwd>врожденные пороки сердца</kwd><kwd>питание</kwd><kwd>нутритивный статус</kwd></kwd-group><kwd-group xml:lang="en"><kwd>children</kwd><kwd>congenital heart diseases</kwd><kwd>nutrition</kwd><kwd>nutritional status</kwd></kwd-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Arodiwe I., Chinawa J., Ujunwa F., Adiele D., Ukoha M., Obidike E. 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