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A rare case of cutaneous mastocytosis in pediatric practice
G. A. Kulakova,
N. A. Solovieva,
S. Ya. Volgina,
E. A. Kurmaeva,
O. V. Kalinina,
I. I. Kaiumova,
L. A. Zarva https://doi.org/10.21508/1027-4065-2023-68-5-119-125
Abstract
Mastocytosis belongs to a group of rare diseases in which there is a pathological accumulation of mast cells in tissues. In childhood, it is more often limited to skin lesions. A clinical case of a bullous form of severe cutaneous mastocytosis, with the onset of the disease at 3.5 months, is presented. Cutaneous manifestations with a positive Darier–Unna symptom and a high level of tryptase in the blood, the exclusion of systemic lesions allowed diagnosing cutaneous mastocytosis and choosing treatment tactics.
About the Authors
G. A. Kulakova
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
N. A. Solovieva
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
S. Ya. Volgina
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
E. A. Kurmaeva
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
O. V. Kalinina
Children’s Polyclinic No.7
Russian Federation
Russian Federation
Kazan
I. I. Kaiumova
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
L. A. Zarva
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
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Review
For citations:
Kulakova G.A., Solovieva N.A., Volgina S.Ya., Kurmaeva E.A., Kalinina O.V., Kaiumova I.I., Zarva L.A. A rare case of cutaneous mastocytosis in pediatric practice. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2023;68(5):119-125. (In Russ.) https://doi.org/10.21508/1027-4065-2023-68-5-119-125
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