

Внезапная сердечная смерть при гипертрофической кардиомиопатии у детей: подходы к профилактике
https://doi.org/10.21508/1027-4065-2024-69-3-6-18
Аннотация
Гипертрофическая кардиомиопатия — основная причина внезапной сердечной смерти у детей и подростков, которая в большинстве случаев обусловлена жизнеугрожающими аритмиями. В статье описаны факторы риска внезапной смерти и освещены основные проблемы профилактики внезапной сердечной смерти у детей с гипертрофической кардиомиопатией. Рассмотрены современные проблемы стратификации риска внезапной сердечной смерти у детей, основанные на оценке факторов риска и многофакторных математических моделях риска. Рассмотрены клинические, функциональные и генетические маркеры риска внезапной смерти у детей в сравнении со взрослой популяцией. Представлены показания к имплантации кардиовертера-дефибриллятора (ИКД) для профилактики внезапной смерти и оценена эффективность ИКД-терапии.
Об авторе
И. В. ЛеонтьеваРоссия
Леонтьева Ирина Викторовна — д.м.н., проф.,
гл. науч. сотр. отдела детской кардиологии и аритмологии; проф. кафедры инновационной педиатрии и детской хирургии
125412 Москва, ул. Талдомская, д. 2
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Рецензия
Для цитирования:
Леонтьева И.В. Внезапная сердечная смерть при гипертрофической кардиомиопатии у детей: подходы к профилактике. Российский вестник перинатологии и педиатрии. 2024;69(3):6-18. https://doi.org/10.21508/1027-4065-2024-69-3-6-18
For citation:
Leontyeva I.V. Sudden cardiac death in children with hypertrophic cardiomyopathy: approaches to prevention. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2024;69(3):6-18. (In Russ.) https://doi.org/10.21508/1027-4065-2024-69-3-6-18