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Внезапная сердечная смерть при гипертрофической кардиомиопатии у детей: подходы к профилактике

https://doi.org/10.21508/1027-4065-2024-69-3-6-18

Аннотация

Гипертрофическая кардиомиопатия — основная причина внезапной сердечной смерти у детей и подростков, которая в большинстве случаев обусловлена жизнеугрожающими аритмиями. В статье описаны факторы риска внезапной смерти и освещены основные проблемы профилактики внезапной сердечной смерти у детей с гипертрофической кардиомиопатией. Рассмотрены современные проблемы стратификации риска внезапной сердечной смерти у детей, основанные на оценке факторов риска и многофакторных математических моделях риска. Рассмотрены клинические, функциональные и генетические маркеры риска внезапной смерти у детей в сравнении со взрослой популяцией. Представлены показания к имплантации кардиовертера-дефибриллятора (ИКД) для профилактики внезапной смерти и оценена эффективность ИКД-терапии.

Об авторе

И. В. Леонтьева
ОСП «Научно-исследовательский клинический институт педиатрии и детской хирургии им. академика Ю.Е. Вельтищева» (Институт Вельтищева) ФГАОУ ВО РНИМУ им. Н.И. Пирогова Минздрава России; ФГАОУ ВО «Российский национальный исследовательский медицинский университет им. Н.И. Пирогова» Минздрава России
Россия

Леонтьева Ирина Викторовна — д.м.н., проф.,
гл. науч. сотр. отдела детской кардиологии и аритмологии; проф. кафедры инновационной педиатрии и детской хирургии

125412 Москва, ул. Талдомская, д. 2



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Рецензия

Для цитирования:


Леонтьева И.В. Внезапная сердечная смерть при гипертрофической кардиомиопатии у детей: подходы к профилактике. Российский вестник перинатологии и педиатрии. 2024;69(3):6-18. https://doi.org/10.21508/1027-4065-2024-69-3-6-18

For citation:


Leontyeva I.V. Sudden cardiac death in children with hypertrophic cardiomyopathy: approaches to prevention. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2024;69(3):6-18. (In Russ.) https://doi.org/10.21508/1027-4065-2024-69-3-6-18

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ISSN 1027-4065 (Print)
ISSN 2500-2228 (Online)