Nutritional Support for Child with Werdnig–Hoffmann Spinal Muscular Atrophy
E. A. Balakireva,
A. V. Slepukhina,
P. V. Serikov,
O. A. Puchenkova,
V. M. Mikhareva,
Yu. A. Bagreeva https://doi.org/10.21508/1027-4065-2020-65-6-72-75
Abstract
Some of the severe manifestations of Werdnig-Hoffmann disease are the pseudobulbar and bulbar syndromes complicated by the hypotrophy of the various degrees of severity. The clinical case of the nutritional support for the child with grade II hypotrophy that complicated the course of Werdnig–Hoffmann disease in one-year-old child is presented. The purpose of this study is to assess the effect of Clinutren Junior high-calorie formula for children from 1 to 10 years of age on the growth and development of the child diagnosed with type I spinal muscular atrophy. The results were analyzed according to the degree of change in the following anthropometric data: mid-arm circumference, mid-hip circumference, the size of the skin fold in the periumbilical region, as well as laboratory data, as follows: albumin, total protein, lymphocytes.
About the Authors
E. A. Balakireva
Belgorod National Research University «Belgorod State University»
Russian Federation
Belgorod
Russian Federation
Belgorod
A. V. Slepukhina
Belgorod National Research University «Belgorod State University»
Russian Federation
Belgorod
Russian Federation
Belgorod
P. V. Serikov
Belgorod National Research University «Belgorod State University»
Russian Federation
Belgorod
Russian Federation
Belgorod
O. A. Puchenkova
Belgorod National Research University «Belgorod State University»
Russian Federation
Belgorod
Russian Federation
Belgorod
V. M. Mikhareva
Belgorod National Research University «Belgorod State University»
Russian Federation
Belgorod
Russian Federation
Belgorod
Yu. A. Bagreeva
Belgorod National Research University «Belgorod State University»
Russian Federation
Belgorod
Russian Federation
Belgorod
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Review
For citations:
Balakireva E.A., Slepukhina A.V., Serikov P.V., Puchenkova O.A., Mikhareva V.M., Bagreeva Yu.A. Nutritional Support for Child with Werdnig–Hoffmann Spinal Muscular Atrophy. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2020;65(6):72-75. (In Russ.) https://doi.org/10.21508/1027-4065-2020-65-6-72-75
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