Emotional and personal characteristics of adolescents with Ehlers–Danlos syndrome
https://doi.org/10.21508/1027-4065-2021-66-2-101-104
Abstract
Hereditary connective tissue diseases are among the most common genetic syndromes. In most cases the studies of children with Ehlers–Danlos syndrome are devoted to the clinical manifestations of the disease. Insufficient information on the features of emotional, personal, and behavioral spheres in this category of children creates the need to perform targeted psychological research.
Objective. To study the features of the emotional and personal sphere in adolescents with Ehlers–Danlos syndrome of 12–16 years old.
Material and methods. The study involved 24 boys and 22 girls from 12 to 18 years old with a clinical diagnosis of Ehlers–Danlos syndrome. The study used multidirectional diagnostic methods of emotional, personal and behavioral spheres.
Results. The emotional features of adolescents with Ehlers–Danlos syndrome are manifested in the form of depressive, anxiety states, which are associated with frustrated needs for self-affirmation. The study revealed the heterogeneity and originality of the picture of emotional and personal characteristics of patients with Ehlers–Danlos syndrome. The degree of awareness of the individual characteristics of a teenager affects the personal development of the child as a whole.
Supporting agencies: The study was carried out within the framework of state Funding «Analysis of clinical and genetic polymorphism of disabled monogenic diseases in children to predict their course and identify molecular targets for optimizing treatment» АААА-А18-118051790107-2.
About the Authors
L. A. Troitskaya
Pirogov Russian National Research Medical University; Scientific and Practical Center for Children’s Psychoneurology
Russian Federation
Russian Federation
Moscow
K. L. Surkova
National Medical Research Center for Children’s Health
Russian Federation
Russian Federation
Moscow
А. N. Semyachkina
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
E. А. Nikolaeva
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
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Review
For citations:
Troitskaya L.A., Surkova K.L., Semyachkina А.N., Nikolaeva E.А. Emotional and personal characteristics of adolescents with Ehlers–Danlos syndrome. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2021;66(2):101-104. (In Russ.) https://doi.org/10.21508/1027-4065-2021-66-2-101-104
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