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Craniofacial polyossal fibrous dysplasia
G. A. Kulakova,
N. A. Solovyeva,
E. A. Kurmaeva,
S. Ya. Volgina,
E. V. Nikiforova,
G. I. Davletshina,
D. O. Kuptsova https://doi.org/10.21508/1027-4065-2022-67-5-199-202
Abstract
Fibrous dysplasia is a rare anomaly of bone tissue development, in which it is replaced by fibrocystic tissue. A clinical case of a patient with a craniofacial polyossal form of fibrous dysplasia is presented. At the age of 13, a child had a constant intense headache, which was accompanied by dizziness, tinnitus, cognitive impairment, deformity of the frontal region and lower jaw on the right, local pigmentation in the neck and face (coffee-and-milk-like stains). Brain tomography and osteoscintigraphy visualized a volumetric formation in the right half of the skull bones, in which fibrotic dysplasia was revealed during histological examination.
Conclusion. To establish this diagnosis, a combination of pain syndrome with deformation of the facial part of the skull and histological examination is important.
About the Authors
G. A. Kulakova
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
N. A. Solovyeva
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
E. A. Kurmaeva
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
S. Ya. Volgina
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
E. V. Nikiforova
Children’s Polyclinic No. 10
Russian Federation
Russian Federation
Kazan
G. I. Davletshina
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
D. O. Kuptsova
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
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Review
For citations:
Kulakova G.A., Solovyeva N.A., Kurmaeva E.A., Volgina S.Ya., Nikiforova E.V., Davletshina G.I., Kuptsova D.O. Craniofacial polyossal fibrous dysplasia. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2022;67(5):199-202. (In Russ.) https://doi.org/10.21508/1027-4065-2022-67-5-199-202
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