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Dystrophic bullous epidermolysis in a newborn
https://doi.org/10.21508/1027-4065-2023-68-5-70-72
Abstract
Congenital bullous epidermolysis is a severe hereditary disease, the main manifestation of which is bubbles that occur after minor mechanical action on the skin and mucous membranes due to congenital violation of the coding of dermo-epidermal proteins. The difficulty in making a diagnosis of congenital bullous epidermolysis is associated with the rarity of pathology and a small number of scientific publications.
About the Authors
A. A. Babintseva
Kazan State Medical University;
City Clinical Hospital №7
Russian Federation
Russian Federation
Kazan
D. I. Sadykova
Kazan State Medical University
Russian Federation
Russian Federation
Kazan
К. О. Zvegintseva
Kazan State Medical University;
City Clinical Hospital №7
Russian Federation
Russian Federation
Kazan
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Review
For citations:
Babintseva A.A., Sadykova D.I., Zvegintseva К.О. Dystrophic bullous epidermolysis in a newborn. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2023;68(5):70-72. (In Russ.) https://doi.org/10.21508/1027-4065-2023-68-5-70-72
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