Репродуктивное здоровье девочек с врожденной гиперплазией коры надпочечников
Аннотация
Врожденная гиперплазия коры надпочечников — группа наследственных заболеваний, связанных с рядом дефектов ферментных систем надпочечников, которые ведут к нарушению полового развития. Заболевания характеризуются триадой обязательных признаков: снижение продукции кортизола, высокое содержание адренокортикотропного гормона в крови, двусторонняя гиперплазия коры надпочечников. В обзоре представлен анализ диагностики врожденной гиперплазии коры надпочечников, а также данные о дисфункции менструального цикла, ведущей к нарушению репродуктивного здоровья девочек.
Об авторах
Л. В. Адамян
Московский государственный медико-стоматологический университет им. А.И. Евдокимова
Россия
акад. РАМН, проф., засл. деятель науки РФ, зам. директора по научной работе Научного центра акушерства, гинекологии и перинатологии им. В.И. Кулакова, зав. кафедрой репродуктивной медицины и хирургии Московского государственного медико-стоматологического университета им. А.И. Евдокимова
Россия
акад. РАМН, проф., засл. деятель науки РФ, зам. директора по научной работе Научного центра акушерства, гинекологии и перинатологии им. В.И. Кулакова, зав. кафедрой репродуктивной медицины и хирургии Московского государственного медико-стоматологического университета им. А.И. Евдокимова
Е. А. Богданова
Московский государственный медико-стоматологический университет им. А.И. Евдокимова
Россия
д.м.н., проф. тойже кафедры
Россия
д.м.н., проф. тойже кафедры
Е. В. Сибирская
Измайловская детская городская клиническая больница, Москва
Россия
Россия
д.м.н., асе. той же кафедры, врач гинекологического отделения Измайловской детской городской клинической больницы Москвы
Т. М. Глыбина
Измайловская детская городская клиническая больница, Москва
Россия
засл. врач Российской Федерации, зав. отделением гинекологии Измайловской детской городской клинической больницы Москвы
Россия
засл. врач Российской Федерации, зав. отделением гинекологии Измайловской детской городской клинической больницы Москвы
М. Б. Гарунова
Московский государственный медико-стоматологический университет им. А.И. Евдокимова
Россия
асп. той же кафедры
Россия
асп. той же кафедры
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Рецензия
Для цитирования:
Адамян Л.В., Богданова Е.А., Сибирская Е.В., Глыбина Т.М., Гарунова М.Б. Репродуктивное здоровье девочек с врожденной гиперплазией коры надпочечников. Российский вестник перинатологии и педиатрии. 2014;59(2):43-47.
For citation:
Adamyan L.V., Bogdanova E.A., Sibirskaya E.V., Glybina T.M., Garunova M.B. Reproductive health of girls with congenital adrenal hyperplasia. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2014;59(2):43-47. (In Russ.)
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