Rapidly progressive idiopathic pulmonary hypertension in a child
Abstract
The diagnosis and therapy of pulmonary hypertension in children are now one of the current acute health problems in the Russian Federation. The purpose of the study was to describe the clinical picture, diagnosis, and treatment of the disease and to attempt to perform specific therapy for rapidly progressive idiopathic pulmonary hypertension and chronic heart failure. Unfortunately, there is now no panacea for treating children with this abnormality. However, current medicamental approaches using specific therapy drugs (endothelin receptor antagonists, phosphodiesterase type 5 inhibitors, prostaglandins) and their combinations offer prospects for the effective treatment of patients and improve prognosis.
About the Authors
D. I. Sadykova
Kazan State Medical University
Russian Federation
Russian Federation
N. N. Firsova
Children`s Clinical Hospital, Kazan
Russian Federation
Russian Federation
A. A. Lobanikhin
Kazan State Medical University
Russian Federation
Russian Federation
A. E. Kalinicheva
Kazan State Medical University
Russian Federation
Russian Federation
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Review
For citations:
Sadykova D.I., Firsova N.N., Lobanikhin A.A., Kalinicheva A.E. Rapidly progressive idiopathic pulmonary hypertension in a child. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2014;59(1):71-75. (In Russ.)
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