Rehabilitation of children with progressive muscular dystrophy Duchenne
Abstract
Duchenne muscular dystrophy is the most common form of myodystrophy characterized by muscle weakness and atrophy and a progressive course due to progressive muscle fiber degeneration. Until now, this disease is regarded as incurable. Patients receive only maintenance therapy aimed at improving the quality of life and preventing complications. The article considers the most relevant methods used in the rehabilitation of children with this pathology. It reviews an update on the impact of physical exercises on dystrophin-deficient muscles. Particular emphasis is placed on the need for further investigations to elaborate specific recommendations for medical staff, patients and their families.
About the Authors
N. Yu. Nikolenko
I.M. Sechenov First Moscow State Medical University
Russian Federation
Russian Federation
O. V. Goncharova
I.M. Sechenov First Moscow State Medical University
Russian Federation
Russian Federation
S. B. Artemyeva
Central Research Institute for Public Health Organization and Informatization, Moscow; Research Clinical Institute of Pediatrics, Moscow
Russian Federation
Russian Federation
E. E. Achkasov
I.M. Sechenov First Moscow State Medical University
Russian Federation
Russian Federation
E. B. Litvinova
Central Research Institute for Public Health Organization and Informatization, Moscow; Research Clinical Institute of Pediatrics, Moscow
Russian Federation
Russian Federation
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Review
For citations:
Nikolenko N.Yu., Goncharova O.V., Artemyeva S.B., Achkasov E.E., Litvinova E.B. Rehabilitation of children with progressive muscular dystrophy Duchenne. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2014;59(4):28-31. (In Russ.)
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