Wilson—Mikity syndrome is a rare chronic neonatal interstitial lung disease
Abstract
The Wilson—Mikity syndrome is a neonatal interstitial lung disease of unknown etiology, which occurs between 1 and 2 months of age and which is characterized by late development of oxygen dependency. The paper gives information on the possible etiological factors, pathogenesis, pathomorphology, and clinical, X-ray, and CT patterns of this rare lung disease. Analysis of 61 cases described in the literature from 1960 to 2008 established the relationship of the manifestations of the syndrome to age and degree of prematurity, as well as disease outcomes. The authors give the results of their observations of 7 patients with Wilson—Mikity syndrome, including the pattern of high-resolution computed tomography.
About the Authors
D. Yu. Ovsyannikov
Peoples’ Friendship University of Russia, Moscow
Russian Federation
Russian Federation
M. V. Narogan
Acad. V.I. Kulakov Research Center of Obstetrics, Gynecology, and Perinatology, Moscow
Russian Federation
Russian Federation
M. A. Belyashova
Peoples’ Friendship University of Russia, Moscow
Russian Federation
Russian Federation
A. A. Krushelnitsky
Peoples’ Friendship University of Russia, Moscow
Russian Federation
Russian Federation
L. D. Vorona
Scientific-and-Practical Center for Health Care to Children with Craniofacial Malformations and Congenital Nervous System Diseases, Moscow
Russian Federation
Russian Federation
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Review
For citations:
Ovsyannikov D.Yu., Narogan M.V., Belyashova M.A., Krushelnitsky A.A., Vorona L.D. Wilson—Mikity syndrome is a rare chronic neonatal interstitial lung disease. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2014;59(4):56-63. (In Russ.)
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