Kazabach–Merritt syndrome without skin manifestations in an infant
https://doi.org/10.21508/1027-4065-2022-67-1-120-124
Abstract
The authors observed Kazabach–Merritt syndrome in an infant with an intrathoracic localization of the tumor without vascular manifestations on the skin. The disease was detected by signs of hemopericardium during screening echocardiography in combination with thrombocytopenia and relapses of intrathoracic bleeding. The diagnosis was confirmed by MSCT and biopsy data. Treatment with beta-blockers and chemotherapy resulted in tumor reduction and the disappearance of clinical symptoms.
About the Authors
O. S. Efremova
Irkutsk State Medical Academy of Continuous Professional Education branch of Russian Medical Academy of Continuous
Professional Education; Regional Children’s Hospital
Russian Federation
Russian Federation
Irkutsk
L. V. Bregel
Irkutsk State Medical Academy of Continuous Professional Education branch of Russian Medical Academy of Continuous
Professional Education; Regional Children’s Hospital
Russian Federation
Russian Federation
Irkutsk
A. E. Matyunova
Irkutsk State Medical Academy of Continuous Professional Education branch of Russian Medical Academy of Continuous
Professional Education
Russian Federation
Russian Federation
Irkutsk
N. Yu. Rudenko
Regional Children’s Hospital
Russian Federation
Russian Federation
Irkutsk
A. O. Barakin
Irkutsk State Medical Academy of Continuous Professional Education branch of Russian Medical Academy of Continuous
Professional Education; Regional Children’s Hospital
Russian Federation
Russian Federation
Irkutsk
T. S. Korinets
Regional Children’s Hospital
Russian Federation
Russian Federation
Irkutsk
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Review
For citations:
Efremova O.S., Bregel L.V., Matyunova A.E., Rudenko N.Yu., Barakin A.O., Korinets T.S. Kazabach–Merritt syndrome without skin manifestations in an infant. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2022;67(1):120-124. (In Russ.) https://doi.org/10.21508/1027-4065-2022-67-1-120-124
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