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Rare variant of heterotaxy syndrome in childhood in pulmonology clinic
Yu. L. Mizernitskiy,
A. A. Novak,
I. E. Zorina,
S. E. Ryabova,
I. A. Kovalev,
E. G. Verchenko,
V. S. Bereznitskiy,
L. P. Melikyan,
L. V. Egorov https://doi.org/10.21508/1027-4065-2022-67-6-88-92
Abstract
Heterotaxy syndrome is a congenital malformation in which the internal organs of the chest and abdominal cavity have an abnormal location. People suffering from this syndrome have multiple complex defects in the heart, blood vessels, spleen, liver, lungs and other organs. Heterotaxy is a rare pathology that requires a multidisciplinary approach to diagnosis. This article demonstrates a rare case of heterotaxy observed in the pulmonology clinic of the Veltischev Institute.
About the Authors
Yu. L. Mizernitskiy
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
A. A. Novak
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
I. E. Zorina
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
S. E. Ryabova
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
I. A. Kovalev
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
E. G. Verchenko
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
V. S. Bereznitskiy
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
L. P. Melikyan
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
L. V. Egorov
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Moscow
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Review
For citations:
Mizernitskiy Yu.L., Novak A.A., Zorina I.E., Ryabova S.E., Kovalev I.A., Verchenko E.G., Bereznitskiy V.S., Melikyan L.P., Egorov L.V. Rare variant of heterotaxy syndrome in childhood in pulmonology clinic. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2022;67(6):88-92. (In Russ.) https://doi.org/10.21508/1027-4065-2022-67-6-88-92
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