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Management of a child with portopulmonal hypertension due to cavernous transformation of the portal vein and sple- norenal anastomosis
E. Yu. Emelyanchik,
N. G. Volf,
T. V. Cherkashina,
E. A. Anikina,
I. Yu. Naumenko,
L. N. Antsiferova,
E. N. Kuzminykh https://doi.org/10.21508/1027-4065-2024-69-1-102-107
Abstract
A clinical case of the development of portopulmonary hypertension in a child after splenorenal anastomosis is presented. The surgical intervention was performed to correct the congenital malformation — cavernous transformation of the portal vein, which led to portal hypertension and varicose veins of the esophagus and stomach. In the long-term postoperative period, pulmonary arterial hypertension, hypersplenism with bilinear cytopenia, and moderate liver failure developed. Combined therapy provided a temporary improvement of the patient status, therefore, during subsequent surgery, the size of the anastomosis was changed. This led to a sustained decrease in pulmonary artery blood pressure and clinical improvement in the boy’s condition.
About the Authors
E. Yu. Emelyanchik
Voino-Yasenetsky Krasnoyarsk State Medical University
Russian Federation
Russian Federation
Krasnoyarsk
N. G. Volf
Krasnoyarsk Regional Clinical Center for Maternal and Child Health
Russian Federation
Russian Federation
Krasnoyarsk
T. V. Cherkashina
Krasnoyarsk Regional Clinical Center for Maternal and Child Health
Russian Federation
Russian Federation
Krasnoyarsk
E. A. Anikina
Krasnoyarsk Regional Clinical Center for Maternal and Child Health
Russian Federation
Russian Federation
Krasnoyarsk
I. Yu. Naumenko
Krasnoyarsk Regional Clinical Center for Maternal and Child Health
Russian Federation
Russian Federation
Krasnoyarsk
L. N. Antsiferova
Krasnoyarsk Regional Clinical Center for Maternal and Child Health
Russian Federation
Russian Federation
Krasnoyarsk
E. N. Kuzminykh
Federal Center for Cardiovascular Surgery
Russian Federation
Russian Federation
Krasnoyarsk
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Review
For citations:
Emelyanchik E.Yu., Volf N.G., Cherkashina T.V., Anikina E.A., Naumenko I.Yu., Antsiferova L.N., Kuzminykh E.N. Management of a child with portopulmonal hypertension due to cavernous transformation of the portal vein and sple- norenal anastomosis. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2024;69(1):102-107. (In Russ.) https://doi.org/10.21508/1027-4065-2024-69-1-102-107
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