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Kasabach—Merritt syndrome caused by portal cavernoma in a 7-year-old boy

https://doi.org/10.21508/1027-4065-2014-59-6-125-135

Abstract

The paper describes the unusual location of cavernous transformation (cavernoma) in the portal vein, which has caused a clinical and hematologic picture of Kazabach—Merritt syndrome and portal hypertension in a 7-year-old boy.

About the Authors

R. G. Artamonov
N.I. Pirogov Russian National Research Medical University, Moscow
Russian Federation


L. V. Glazunova
Morozov City Children's Clinical Hospital, Moscow
Russian Federation


E. S. Busova
Morozov City Children's Clinical Hospital, Moscow
Russian Federation


M. V. Polyakov
N.I. Pirogov Russian National Research Medical University, Moscow
Russian Federation


N. I. Kirnus
N.I. Pirogov Russian National Research Medical University, Moscow
Russian Federation


References

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Review

For citations:


Artamonov R.G., Glazunova L.V., Busova E.S., Polyakov M.V., Kirnus N.I. Kasabach—Merritt syndrome caused by portal cavernoma in a 7-year-old boy. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2014;59(6):106-108. (In Russ.) https://doi.org/10.21508/1027-4065-2014-59-6-125-135

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ISSN 1027-4065 (Print)
ISSN 2500-2228 (Online)