Hamman–Rich syndrome in a young child
https://doi.org/10.21508/1027-4065-2019-64-4-83-87
Abstract
Hamman–Rich syndrome (idiopathic fibrosing alveolitis) is a lung disease of unknown nature, characterized by non-infectious inflammation of the interstitium, alveoli and terminal bronchioles with an outcome in progressive pulmonary fibrosis. Idiopathic fibrosing alveolitis in young children, despite the timely verification of the diagnosis and therapy, is characterized by an unfavorable prognosis and rapidly progressive course. The article describes the clinical case of Hamman–Rich syndrome in a child of 8 months, its main clinical manifestations and diagnostic features.
About the Authors
T. A. Minenkova
Kursk State Medical University
Russian Federation
Kursk
Russian Federation
Kursk
Yu. L. Mizernitsky
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Moscow
Russian Federation
Moscow
N. S. Razinkova
Kursk State Medical University
Russian Federation
Kursk
Russian Federation
Kursk
A. V. Serezhkina
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Moscow
Russian Federation
Moscow
M. V. Kostyuchenko
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Moscow
Russian Federation
Moscow
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Review
For citations:
Minenkova T.A., Mizernitsky Yu.L., Razinkova N.S., Serezhkina A.V., Kostyuchenko M.V. Hamman–Rich syndrome in a young child. Rossiyskiy Vestnik Perinatologii i Pediatrii (Russian Bulletin of Perinatology and Pediatrics). 2019;64(4):83-87. (In Russ.) https://doi.org/10.21508/1027-4065-2019-64-4-83-87
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